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It is possible that the main title of the report Ramsay Hunt Syndrome is not the name you expected. Please check the synonyms listing to find the alternate name(s) and disorder subdivision(s) covered by this report.
Ramsay Hunt syndrome (RHS) is a rare neurological disorder characterized by paralysis of the facial nerve (facial palsy) and a rash affecting the ear or mouth. Ear abnormalities such as ringing in the ears (tinnitus) and hearing loss may also be present. Ramsay Hunt syndrome is caused by the varicella zoster virus (VZV), the same virus that causes chickenpox in children and shingles (herpes zoster) in adults. In cases of Ramsay Hunt syndrome, previously inactive (dormant) varicella-zoster virus is reactivated and spreads to affect the facial nerve.
Several different names have been used to denote this disorder in the medical literature often causing confusion. The disorder is named after James Ramsay Hunt, a physician who first described the disorder in 1907. Year agos, more than one disorder bore the designation Ramsay Hunt syndrome. Ramsay-Hunt syndrome is now used to denote the disorder described in this report. The disorder is also sometimes known as herpes zoster oticus because of the characteristic ear rash. However, some physicians use herpes zostic oticus only for the ear rash and Ramsay Hunt syndrome for the combination of ear rash and facial paralysis.
American Pain Society
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National Shingles Foundation
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Genetic and Rare Diseases (GARD) Information Center
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Center for Peripheral Neuropathy
University of Chicago
5841 South Maryland Ave, MC 2030
Chicago, IL 60637
American Academy of Audiology
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Reston, VA 20190
This is an abstract of a report from the National Organization for Rare Disorders (NORD). A copy of the complete report can be downloaded free from the NORD website for registered users. The complete report contains additional information including symptoms, causes, affected population, related disorders, standard and investigational therapies (if available), and references from medical literature. For a full-text version of this topic, go to www.rarediseases.org and click on Rare Disease Database under "Rare Disease Information".
The information provided in this report is not intended for diagnostic purposes. It is provided for informational purposes only. NORD recommends that affected individuals seek the advice or counsel of their own personal physicians.
It is possible that the title of this topic is not the name you selected. Please check the Synonyms listing to find the alternate name(s) and Disorder Subdivision(s) covered by this report
This disease entry is based upon medical information available through the date at the end of the topic. Since NORD's resources are limited, it is not possible to keep every entry in the Rare Disease Database completely current and accurate. Please check with the agencies listed in the Resources section for the most current information about this disorder.
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Last Updated: 2/4/2011
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